Recent studies and trials have demonstrated significant advancements in gene therapy as a treatment for inherited deafness, particularly for OTOF-related and DFNB9 types. A multicentre trial has revealed that gene therapy improves hearing in 90% of patients, with impressive results sustained for over two years. The findings underscore the potential of gene therapy to restore hearing, marking a pivotal moment in the treatment of deafness and offering hope to many affected individuals.